SKU: 20354459837

Osteogenesis Imperfecta (OI)

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Description

Osteogenesis Imperfecta (OI)Osteogenesis imperfecta (OI) ist eine erbliche autosomal rezessive Erkrankung, die durch extrem fragile Knochen und Zhne gekennzeichnet ist. Klinische Anzeichen umfassen Schmerzen, spontane Frakturen von Knochen und Zahnfrakturen, Gelenkhyperlaxitt und reduzierte Knochendichte in der Rntgenaufnahme. Die Zhne sind sehr dnn und zerbrechlich, ansonsten normal gro. Bei betroffenen Hunden treten die klinischen Anzeichen innerhalb der ersten Lebenswochen

Osteogenesis imperfecta (OI) ist eine erbliche autosomal-rezessive Erkrankung, die durch extrem fragile Knochen und Zähne gekennzeichnet ist. Klinische Anzeichen umfassen Schmerzen, spontane Frakturen von Knochen und Zahnfrakturen, Gelenkhyperlaxität und reduzierte Knochendichte in der Röntgenaufnahme. Die Zähne sind sehr dünn und zerbrechlich, ansonsten normal groß. Bei betroffenen Hunden treten die klinischen Anzeichen innerhalb der ersten Lebenswochen auf. OI ist gekennzeichnet durch eine signifikante Reduktion der Bildung von Knochen- und Zahnmasse (Osteopenie und Dentinopenie) aufgrund eines Defekts in der Bildung von Kollagen Typ I. Kollagen Typ I macht 90 % des organischen Materials von Knochen, Sehnen und Zähnen aus. Während es diesen Organen Struktur und Elastizität verleiht, führen die Defekte im Kollagen zu Zerbrechlichkeit.

Der Grund für das Auftreten von OI bei bestimmten Hunderassen sind Mutationen in den Genen, die Untereinheiten von Kollagen I kodieren. Während bei Dackeln die Ursache der OI die Mutation im Gen SERPINH1 ist, das an der Bildung von Kollagen I beteiligt ist. Das von diesem Gen kodierte Protein ist an der korrekten Faltung der Kollagen-Dreifachhelix beteiligt. Defekte der hochorganisierten Struktur der Kollagen-Dreifachhelix führen zu Osteogenesis imperfecta.

Vererbung: autosomal-rezessiv

Mutation: SERPINH1 Gen

Gentest: Die verwendete Methode zum Testen ist extrem genau und ermöglicht eine vollständige Differenzierung zwischen betroffenen Tieren, Trägern und gesunden Hunden. Der Test kann in jedem Alter durchgeführt werden.

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SKU: 20354459837

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4.6 ★★★★★
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Megan
Omaha, US
★★★★★ 5
Sturdy and Functional
Color: White, Size: 4 Panel Basic
I got this to replace a poor quality divider that I tried first, and this thing is the best! It is easily folded, stands sturdily, easy to assemble, and the fabric looks great. Very very happy with the quality for the price.
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Reviewed in the United States on March 17, 2026
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L. E. Morales
Phoenix, US
★★★★★ 1
Arrived damaged
Color: Black, Size: 4 Panel Basic
Unfortunately, very cheaply made. It arrived with one of the connecting tubes cracked horizontally. Possibly due to bad welding. It is quite a headache to assemble. It was delivered on time but returned for a refund.
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Reviewed in the United States on April 8, 2026
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Elisabeth Baird Bennett
Houston, US
★★★★★ 3
Not a great experience but a fine product
Color: Black, Size: 4 Panel Basic
not enough screws were included to make the wall. I was able to locate more screws to finish building-so I didn’t have to return the product- but it was a pain and I got lucky finding the pieces I needed but it could’ve been a fail and a returned product
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Reviewed in the United States on January 12, 2026
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April Lehman
Belleville, US
★★★★★ 5
Useful, simple room divider
Color: White, Size: 4 Panel Basic
All the pieces were accounted for, and some even had extra pieces, maybe just in case they need changing. It was a bit like putting together a piece of IKEA furniture, though I went slower than usual so as not to make any mistakes. It wasn’t too hard to put together myself, and helps give my studio apt a feeling of space and privacy for my bed. I only wish it had a lovely Japanese design on it, but it does amazingly seem to match the wall color.
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Reviewed in the United States on March 3, 2026
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Kswain149
Lexington, US
★★★★★ 4
Multi purpose divider
Color: White, Size: 4 Panel Basic
I am excited this divider is being used to block off a portion of the dining room where I stored extra supplies. It looks nice!
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Reviewed in the United States on October 1, 2025

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